mayor rokitansky syndrome (Vaginal Orifice)

Vaginal Orifice in a case of Mayer-Rokitansky Syndrome I came across during my Housestaffship Training in G&O. Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome consists of vaginal aplasia with other müllerian (ie, paramesonephric) duct abnormalities. Signs and symptoms: The patient undergoes puberty with normal thelarche and adrenarche; however, menses do not begin (ie, primary amenorrhea) Patients may report cyclic abdominal pain due to cyclic endometrial shedding without a patent drainage pathway Because ovarian function is normal, patients experience all bodily changes associated with menstruation Infertility Difficulty with intercourse Voiding difficulties, urinary incontinence, or recurrent UTIs Vertebral anomalies (most commonly scoliosis) The degree of vaginal aplasia can vary from complete absence to a blind pouch. The more shallow the canal, the greater the likelihood of the patient having dyspareunia or inability to have intercourse. Physical examination findings are as follows: Normal secondary female sexual characteristics are present after puberty Height is normal Speculum examination of the vagina may be impossible or difficult because of the degree of vaginal agenesis The vulva, labia majora, labia minora, and clitoris are normal A palpable sling of tissue may be present at the level of the peritoneal reflection Surgical correction of the vaginal anomaly permits normal sexual function and, possibly, reproduction with assisted techniques.